تأثير علاج هرمون النمو على الطول لدى الأطفال المصابين بالكساح الناقص الفوسفات المرتبط بالكروموسوم X

المؤلفون

DOI:

https://doi.org/10.32007/jfacmedbaghdad.6632349

الكلمات المفتاحية:

Growth hormone، Rickets، Short stature ، X-linked dominant، X-Linked Hypophosphatemic.

الملخص

الكساح الناقص الفوسفات المرتبط بـ X (XLHR) هو الشكل الأكثر شيوعًا للكساح الموروث. عند الأطفال، غالبًا ما يكون توقف النمو وقصر القامة بشكل غير متناسب من العلامات المبكرة لـ XLHR. قد يستمر تأخر النمو حتى بعد تلقي العلاج التقليدي المناسب (مكملات الفوسفات ونظائرها النشطة من فيتامين د)، حتى لو بدأ في وقت مبكر من مرحلة الطفولة. في الآونة الأخيرة، وبغض النظر عن المرض الذي يتم التحكم فيه جيدًا، تم اقتراح العلاج بهرمون النمو البشري المؤتلف (rhGH) كوسيلة فعالة لدعم النمو لدى الأطفال الذين يعانون من XLHR الذين يظهرون نقصًا في النمو. من الضروري المتابعة حتى الوصول إلى ارتفاع البالغين لتقييم التأثيرات طويلة المدى لعلاج هرمون النمو على الارتفاع النهائي.

التنزيلات

تنزيل البيانات ليس متاحًا بعد.

المراجع

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Growth hormone, Rickets, Short stature , X-linked dominant, X-Linked Hypophosphatemic.

التنزيلات

منشور

2024-10-01

كيفية الاقتباس

1.
Al-Zubaidi MA, Abdullah WH. تأثير علاج هرمون النمو على الطول لدى الأطفال المصابين بالكساح الناقص الفوسفات المرتبط بالكروموسوم X. J Fac Med Baghdad [انترنت]. 1 أكتوبر، 2024 [وثق 21 ديسمبر، 2024];66(3):393-7. موجود في: https://iqjmc.uobaghdad.edu.iq/index.php/19JFacMedBaghdad36/article/view/2349

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